内淋巴囊肿瘤患者的临床听力学特征分析

Characteristics of clinical audiology in patients with endolymphatic sac tumor FENG Bo

目的分析内淋巴囊肿瘤患者的临床听力学特征。方法回顾性分析我院1999-2011年收治的16例经病理学和免疫组织化学证实的内淋巴囊肿瘤患者的临床资料。结果本组16例均有不同类型和程度的听力下降,主要表现为全聋、高频率段听力丧失、极重度感音神经性聋、混合性聋和轻度传导性聋。其中9例做声导抗测试,患耳鼓室曲线A型4例,B型1例,C型4例,其鼓室压为-130^-220 daPa;镫骨肌声反射未引出8例,引出1例。结论内淋巴囊肿瘤患者有不同程度听力损失,其程度与肿瘤的范围、侵袭方向、中耳及内耳的受累程度有密切关系,与病程长短也有一定关系。

Objective To analyze the characteristics of clinical audiology in patients with endolymphatic sac tumor（ELST）.Methods The clinical data about 16 patients with pathology and immunohistochemistry-confirmed ELST admitted to our hospital from 1999 to 2011 were retrospectively analyzed.Results Different types and severities of hearing impairment were detected in the 16 patients,which were mainly manifested as total deafness,hearing loss in high frequency band,profound sensorineural hearing loss,mixed hearing loss and mild conductive hearing loss.Of the 9 patients who underwent tympanogram test,4 were diagnosed with type A tympanic curve,one with type B tympanic curve and 4 with type C tympanic curve with a tympanic pressure of-130—220 daPa,and 8 without acoustic reflex and 1 with acoustic reflex.Conclusion Patients with ELST have different types and severities of hearing loss.The severity of hearing loss is closely related with the tumor invasion size and direction,involvement of middle and inner ear,and the course of ELST.