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重视儿科重症监护病房危重噬血细胞综合征的诊断与救治 被引量：2

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摘要 噬血细胞综合征（hemophagocyticsyndrome，HPS）又称噬血细胞淋巴组织细胞增生症（hemophagocyticlymphohistiocytosis，HLH），表现为急性发病，以发热、肝脾肿大、全血细胞减少、急性肝功能障碍、凝血功能异常以及中枢神经系统损害表现为特征，实验室检查血清铁蛋白显著增高，骨髓检查可见噬血细胞，经常在短时间内发展为多器官功能障碍综合征（multipleorgandysfunctionsyndrome，MODS），病死率高[1]。
作者 张育才 崔云
机构地区 上海交通大学附属儿童医院重症医学科
出处 《中华急诊医学杂志》 CAS CSCD 北大核心 2013年第5期456-458,共3页 Chinese Journal of Emergency Medicine
基金 上海市科委科技攻关项目（12411952404）
关键词 噬血细胞综合征 儿科重症监护病房 噬血细胞淋巴组织细胞增生症 多器官功能障碍综合征 中枢神经系统损害 急性肝功能障碍 救治 诊断
分类号 R725.5 [医药卫生—儿科]
  • 相关文献

参考文献14

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二级参考文献47

  • 1郭霞,李强,周晨燕.儿童噬血细胞综合征41例临床分析[J].中华血液学杂志,2007,28(7):449-453. 被引量：26
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共引文献100

同被引文献31

  • 1Willars C. Update in intensive care medicine: acute liver failure. initial management, supportive treatment and who to transplant [J]. Curr Opin Crit Care, 2014, 20 (2) : 202-209.
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  • 8Mindikoglu AL, Magder LS, Regev A. Outcome of liver transplantation for drug-induced acute liver failure in the United States: analysis of the United Network for Organ Sharing database [J]. Liver Transpl, 2009, 15 (7) : 719-729.
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  • 10Gilroy RK, Mailliard ME, Gollan JL. Gastrointestinal disorders of the critically ill: cholestasis of sepsis [ J 1. Best Pract Res Clin Gastroenterol, 2003, 17 (3) : 357-367.

引证文献2

二级引证文献7

中华急诊医学杂志
2013年 第5期

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