出血型烟雾病的研究进展

Research Progress of Hemorrhagic Moyamoya Disease

烟雾病是一种以颈内动脉末端狭窄、闭塞并伴有颅底异常血管网形成为特征的脑血管病,出血型烟雾病是其中的一个重要类型,也是目前的研究热点,本文就出血型烟雾病的流行病学特征、病因及发病机制、影像学特征及预测出血的指标、治疗和疗效评价等做一综述。

Moyamoya disease is a cerebrovascular disease characterized by progressive stenosis or occlusion of the terminal portion of internal carotid arteries and the formation of vascular networks at the base of the brain. Hemorrhagic moyamoya disease, as an important type of this disease, is a research focus now. In this paper, we review the epidemiological characteristics, etiology and pathogenesis, imaging features and the predictor of hemorrhage, its treatment and effectiveness evaluation.