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64例骨髓噬血细胞现象的回顾性分析

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摘要 噬血细胞综合征(hemophagocytic syndrome,HPS)又称噬血细胞性淋巴组织细胞增多症(HLH),是一组因遗传性或获得性免疫缺陷导致的以过度炎症反应为特征的疾病,其临床表现为持续发热,肝脾淋巴结肿大,全血细胞减少,皮疹出血,肝功能异常,凝血障碍,骨髓出现噬血现象。该病临床表现多样,缺乏特异性,容易误漏诊,
出处 《实验与检验医学》 CAS 2013年第4期376-377,共2页 Experimental and Laboratory Medicine
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