Caroli病的诊断与外科治疗(附5例报告)

Diagnosis and treatment of Caroli's disease:Report of 5 cases

目的 :探讨Caroli病的临床特点、分型及诊治原则。方法 :对收治的 5例Caroli病进行回顾性分析 ,并结合文献复习对该病的临床特征、分类方法、影像学诊断以及手术治疗方法进行分析讨论。结果 :该病以年青患者、反复胆管炎及多次手术未能解除胆管感染为特征 ,黄氏四型分类法对术式选择有指导意义 ;B超、CT及MRCP对病变部位、大小及有无结石定位准确 ,尤其是MRCP的三维成像可显示胆管全貌 ;病变切除 (肝叶、胆总管囊肿 )及通畅的胆管引流疗效满意。结论 :根据临床特点及丰富的影像学检查 ,诊断并不困难 ,尤其MRCP在Caroli病诊断中值得推荐 ;依病变类型不同术式选择应个体化 ,随访疗效良好。

Objective:[WT5BZ]To investigate the diagnosis and treatment of Caroli's disease.[WT5HZ]Methods:[WT5BZ]With the review and a retrospective survey of Caroli's disease to five patients treatment in our department,the clinical features,classification,the method of imaging diagnosis and operation were discussed.[WT5HZ]Results:[WT5BZ]The typical clinical feature of Caroli's disease was repeated cholangitis and reoperation in bile duct on youngster patient;The four types classification of Huang Zhi-qiang was fine in instructing the choice of operative methods;the B-mode ultrasonography,computed tomography and magnetic resonance cholangiopancreatogrphy could located the bile duct cysts and stone accurately.Follow-up showed that excision of hepatic lobus(segments)and congenital choledochal cyst with cholangiojejunostomy have been associated with better results.[WT5HZ]Conclusion:[WT5BZ]It was not difficult for the diagnosis of Caroli's disease to depend on abundant imaging examination,however,it was hard for treatment,Operation method was individualize depending on the type of congenital bile duct cysts. [WT5HZ]