以皮疹为首发表现的真性红细胞增多症1例
摘要
真性红细胞增多症（polyeythemia vera，PV）为发病率较低的造血系统疾病。其造血干／祖细胞具有异常克隆性、高增殖性及低凋亡性。临床表现以红细胞增多为主的两系或三系血细胞增多。以及由此引起的血液粘滞表现．其有转化为骨髓纤维化或白血病。的风险。以皮肤病为首发表现的PV病例较少见，现报道1例。
出处
《中国麻风皮肤病杂志》
2013年第9期591-593,共3页
China Journal of Leprosy and Skin Diseases
参考文献7
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共引文献14
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