原发性脊髓黏液乳头型室管膜瘤的诊断和治疗

Diagnosis and treatment of primary spinal myxopapillary ependymoma

目的探讨原发性脊髓黏液乳头型室管膜瘤的临床特征和手术治疗。方法回顾性分析复旦大学附属华山医院神经外科2008年1月至2012年12月收治的18例原发l生脊髓黏液乳头型室管膜瘤的临床特点、诊断、手术治疗及预后。结果本组18例患者手术全切除15例，次全切除3例。术后均未行放疗和化疗。术后15例获得随访，平均随访32个月，无术后复发、转移及死亡病例。结论原炭陛脊髓黏液乳头型室管膜瘤为少见类型室管膜瘤，遵循正确、合理的操作方法全切后可获得良好预后。

Objective To investigate the clinical characteristics and treatment of primary spinal myxopapaillary ependymoma. Methods The clinical features, diagnosis, surgical treatment, and prognosis of 18 patients with primary spinal myxopapillary ependymoma treated at Huashan Hospital of Fudan University during January 2008 to December 2012 were analyzed retrospectively. Results In our series, gross total removal was achieved in 15 patients and subtotal removal in 3 patients. All patients received no radiotherapy and chemotherapy. The mean follow - up period was 32 months in 15 patients. There was no recurrence, metastasis,and death. Conclusions Primary spinal myxopapillary ependymoma is a rare type ependymoma. A better prognosis can be obtained after gross total remove according to correct and rational method of operation.