肺血管外皮瘤一例并文献复习

Pulmonary Hemangiopericytoma: A Case Report and Literature Review

目的提高对肺血管外皮瘤的认识。方法结合1例肺血管外皮瘤患者的临床资料,并复习国内外相关文献,分析、归纳该病的病因、临床表现、影像学特点、病理学特征、诊断标准、治疗方法及预后。结果该病病因不清,临床症状较少且缺乏特异性。影像学检查主要表现为单个圆形巨大软组织肿块,部分分叶,内无钙化。病理学检查主要特征是丰富的毛细血管腔,肿瘤可有假包膜包裹或向周围组织呈浸润性生长。诊断依靠影像学表现,确诊依据病理。治疗首选手术,辅以放、化疗。预后介于良、恶性肿瘤之间。结论肺血管外皮瘤罕见,极易误诊,应充分认识该病的相关表现,提高诊治效果,改善预后。

Objective To enhance the understanding of pulmonary hemangiopericytoma. Methods With a case report and reviewing related literatures, the etiology, clinical manifestations, radiological features, pathological features, diagnosis, treatment and prognosis of pulmonary hemangiopericytoma were discussed. Results The etiology of this rare disease remains unknown. Clinical symptoms are rare and non-specific. Radiological features show a round, homogeneous, soft-tissue mass without calcification. Pathologic feature reveals a large number of capillary lumen, and some tumors can be dressed with pseudo capsule or show infiltration growth to the surrounding tissue. The diagnosis of pulmonary hemangiopericytoma is mainly based on the imaging findings, and pathological examination is needed for final diagnosis. The best choice of treatment is surgery, combined with chemotherapy and radiotherapy. Conclusions Pulmonary hemangiopericytoma is rare and often misdiagnosed as other pulmonary diseases. More attention should be paid to improve its therapeutic： effect and prognosis.