视-隔发育不良的CT和MRI表现

CT and MRI diagnosis of septo-optic dysplasia

目的:探讨视-隔发育不良的CT、MRI影像特征。方法:回顾性分析经临床、影像证实的9例视-隔发育不良患者的CT、MRI表现,4例行CT扫描,5例行MRI扫描,常规行横轴面、矢状面及冠状面扫描。结果:影像学主要表现为透明隔缺如,双侧侧脑室融合,侧脑室前角呈方形,视神经、视交叉和视神经管发育不良,合并脑裂、脑白质发育不良、胼胝体发育不良、小脑发育不良、垂体后叶缺如等畸形。结论:视-隔发育不良的CT、MRI表现具有特征性,MRI对视路的观察优于CT,对于轻度视神经发育不良者需结合眼科检查。

Objective：To explore the CT and MRI imaging features of septo-optic dysplasia. Methods：CT and MR im- ages of nine patients with septo-dysplasia confirmed by clinical diagnosis were analyzed retrospectively,including CT axial scan in four cases and MRI transverse, sagittal coronal scans in the other five cases. Results：CT and MR imaging features of the patients mainly included septum pellucidum absence,bilateral lateral ventricle fusion, square anterior horn of the lateral ventricle,optic nerve,optic chiasm and optic canal dysplasia, some cases combined with scbizencephaly, hypoplasia of white matVer,corpus callosum and cerebellum and the H HL absence in some cases. Conclusion： Septo-opdc dysplasia has obvious imaging features, MRI is better than CT in visual pathway display. For mild cases of optic nerve hypoplasia combination of CT or MRI with ophthalmologic examination needed.