肺母细胞瘤的研究进展

Research advance on pulmonary blastoma

肺母细胞瘤是一种罕见肺部原发恶性肿瘤,分为成人型肺母细胞瘤和儿童胸膜肺母细胞瘤。肺母细胞瘤的临床症状及影像学检查无特异性,容易误诊,术前诊断困难,术后病理需结合形态学和免疫组化综合考虑。本病首选手术治疗,手术方式以肺叶切除加纵隔淋巴结清扫术为主。预后与病理类型、分期及肿瘤部位等有关,总体预后差。

Pulmonary blastoma（PB） is a rare primary malignancy of the lung. It includes two forms-adult type pul- monary blastoma and childhood pleuroplumonary blastoma. Due to non - specificity in clinical characateritics and ico- nography, PB is difficult to be diagnosed before operation. Morphalogical features and immunohistochemial presenta- tion should be analyzed together in postoperative pathological diagnosis. The main treatment for PB is surgery consis- ting of lobectomy or pneumonectomy and dissection of diaphragm lymphnodes. The progonosis is related with the path- ological type,stage and the location of tumor. Overeall.it＇s oroanosis is ooor.