增殖性化脓性口炎

Pyodermatitis-pyostomatitis vegetans

增殖性化脓性口炎(PD-PSV)是一种少见的累及皮肤黏膜的脓疱性和增生性疾病,与炎性肠炎相伴发,因而PD-PSV临床报道少,极其容易误诊。本文检索数十年间所报道的34例PD-PSV患者,从历史沿革、流行病学、临床表现、组织病理学特征、治疗和鉴别诊断等方面进行综述。

Pyodermatitis-pyostomatitis vegetans is a rare disorder characterized by pustular eruption in the oral mucosa and vegetating plaques in the skin. It is associated with inflammatory bowel disease. Because there have been only a few cases described in the published work, the condition is prone to giving erroneous impression leading to delayed or inappropriate treatment. The 34 cases described in the published work for decades were reviewed for the history, epidemiology, clinical feature, treatment and differential diagnosis.