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遗传性多发性骨软骨瘤的影像学分析

Imaging analysis of hereditary multiple exostoses
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摘要 目的:研究遗传性多发性骨软骨瘤(HMO)影像特点。方法:分析经病理证实不同年龄、不同部位的56例HMO影像及家族史。结果:58例HMO疾病患者中,男38例,女20例,其中胫骨及股骨多发,并且对称存在18例,双手及腕关节次之10例,肱骨4例,尺桡骨9例,肋骨3例,骨盆9例,肩胛骨7例;跟骨部位1例。结论:遗传性多发性骨软骨瘤是一种常见的骨良性肿瘤,以股骨下端和胫骨上端好发,其次为长骨端,其有典型遗传倾向,瘤骨发生部位具有家族倾向性。 Objective:To study the hereditary multiple exostoses (hereditary multiple osteoehondroma,HMO) imaging features. Methods:56 cases of HMO confirmed by pathology image and family history in different parts of different age,analysis.Results of the 58 patients with HMO disease patients,male 38 cases,female 20 eases,of which the tibia and femur and muhiple,symmetric about 18 cases,hands and wrist joints of 10 cases,4 cases of humerus,ulna and radius of 9 cases, 3 cases of rib,pelvic in 9 cases,7 cases of scapula,1 cases of caleaneus;conelusion of hereditary multiple exostoses is a common benign bone tumor of distal femur and proximal tibia,with good hair,followed by the end of the long bones,a typical genetic predisposition,tumor bone site with familial tendencies.
作者 王凤娟
出处 《中国社区医师(医学专业)》 2013年第21期78-79,共2页
关键词 遗传性 多发性骨软骨瘤 影像分析 hereditary multiple exostoses imaging analysis
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