以少见表现为首发症状的9例嗜铬细胞瘤临床分析

Nine cases of pheochromocytoma with rare initial clinical manifestations

目的:探讨以少见表现为首发症状的的嗜铬细胞瘤的临床特点。方法:回顾性分析经手术病理证实为嗜铬细胞瘤并具有特殊临床表现的9例患者的临床资料。结果:2例患者术前诊断为急性冠脉综合征;2例患者术前诊断休克;1例患者术前诊断为糖尿病酮症酸中毒;4例患者术前诊断为视神经炎。所有患者均有高血压。影像学检查均发现肾上腺占位病变,均经手术病理证实为肾上腺嗜铬细胞瘤,术后症状好转。结论:嗜铬细胞瘤表现多样化,高血压是重要的诊断线索,实验室及影像学检查对明确诊断有重要意义。

Objective ： To discuss the clinical characteristics of 9 cases of pheochromocytoma with rare clinical manifestation as the initial symptoms. Methods： The clinical data of 9 cases of pheochromocytoma confirmed by operation and pathological finding were analyzed retrospectively. Results： Two cases were diagnosed as acute coronary syndrome, 2 as shock, 1 as diabetic ketoacidosis and 4 as optic neuritis before operation. All patients suffered from hypertension. Imaging studies revealed adrenal mass. All cases were confirmed as adrenal pheochromocytoma by operation and pathological examination. Clinical symptoms of 9 cases were improved after operation. Conclusion ： The clinical manifestations of pheochromocytoma are multiplicity, hypertension is an important diagnostic clue, laboratory and imaging exmninations are crucial for the diagnosis of pheochromocytoma.