摘要
Pulmonary agenesis is a rare congenital malformation of unknown etiology that is defined as the complete absence of the bronchus,lung parenchyma,and pulmonary vasculature.The exact incidence of this rare abnormality is not known but is believed to range from 0.003 4% to 0.009 7%.1 Pulmonary agenesis affects men and women almost equally.Left sided agenesis is more common.More than half of the reported cases are associated with anomalies involving cardiovascular,gastrointestinal,skeletal,and urogenital systems and patients die within the first five years of life.Although some cases are compatible with long-term survival and normal growth,completely symptom free and well tolerated surgery is extremely rare.Here we present a case of congenital left lung agenesis in an adult woman tolerating general anesthesia well for modified radical mastectomy.
Pulmonary agenesis is a rare congenital malformation of unknown etiology that is defined as the complete absence of the bronchus,lung parenchyma,and pulmonary vasculature.The exact incidence of this rare abnormality is not known but is believed to range from 0.003 4% to 0.009 7%.1 Pulmonary agenesis affects men and women almost equally.Left sided agenesis is more common.More than half of the reported cases are associated with anomalies involving cardiovascular,gastrointestinal,skeletal,and urogenital systems and patients die within the first five years of life.Although some cases are compatible with long-term survival and normal growth,completely symptom free and well tolerated surgery is extremely rare.Here we present a case of congenital left lung agenesis in an adult woman tolerating general anesthesia well for modified radical mastectomy.
