左室心肌致密化不全合并先天性左室-右房通道1例

Left ventricular non-compaction and left ventricular-right atrium communication

1病例资料 患者，男，57岁，工人，主因“反复呼吸困难10年余”入院。患者10年前开始出现活动时呼吸困难，伴乏力，偶有夜间平卧受限，无胸痛及肩背部放射痛，无咳嗽及咳粉红色泡沫痰，无双下肢水肿，曾就诊于当地医院，诊断为“冠心病、心功能不全”，给予阿司匹林片、美托洛尔、呋塞米等治疗，症状有所缓解。入院前1个月，患者上述症状加重，

A male patient, 57 years old, was admitted on May. 6, 2013 because of ＂repeated chest tightness and short of breath for 10 years＂. In the past 10 years, the patient had developed chest tightness, short of breath and cough after activities without chest pain. Coronary angiography and left ventriculography showed 30% steno- sis in mid left anterior descending （LAD）, the left ventricular was significantly dilated, the contraction of apex was weakened, EF~_~40~~o MRI showed ventricular wall motion decreased, non densification/densification myo- cardial thickness= 2.5, left ventricular-right atrium communication. The diagnosis is left ventricular non-compaction and left ventricular-right atrium communication.