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合并肺部病变的Good综合征三例并文献复习 被引量：6

Good＇s syndromewithpulmonarylesions：3casereportswithliteraturereview
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摘要 回顾性分析3例合并肺部病变的Good综合征患者临床资料,并结合文献复习总结该病临床表现、肺部病变特征及诊断治疗.3例患者无显著的低γ球蛋白血症,但外周血淋巴细胞亚群检测均可见不同程度异常.胸腺瘤患者出现反复呼吸道感染时应考虑Good综合征的可能,Good综合征可出现弥漫性泛细支气管炎样肺部表现,也可表现为间质性肺病,早期进行免疫状况筛查、积极纠正原发免疫缺陷对改善预后有益. ThreecasesofGoodssyndromewithpulmonarylesionsinourhospitalfromJune1,2010toJune1,2013wereretrospectiveanalyzedandrelevantliteratureswerereviewed.Clinicalmanifestation,characteristicsofpulmonarylesions,diagnosisandtreatmentweresummarized.Abnormalityoflymphocytesubpopulationtovaryingdegreesinperipheralbloodwasdetectedinall3cases.Howevernoneshowedhypogammaglobulinemia.Ifthymomapatientsdevelopedrecurrentrespiratoryinfections,Good＇s syndromeshouldbeconsidered.PulmonarymanifestationsofGoodsyndromehavelesionssimilartothoseofdiffusepanbronchiolitisorinterstitiallungdisease.Earlyscreeningofimmunecompetencyandtreatmentforimmunodeficiencymayimproveprognosis.
作者 李冉 马艳良 魏敬安 韩芳 曹照龙 高占成
机构地区 北京大学人民医院呼吸与危重症医学科
出处 《中华全科医师杂志》 2014年第4期308-310,共3页 Chinese Journal of General Practitioners
基金 国家科技支撑计划课题（2012BA105802）
关键词 胸腺瘤相关免疫缺陷综合征肺疾病 Good＇s syndrome Lungdiseases
分类号 R736.3 [医药卫生—肿瘤]
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参考文献4

二级参考文献25

  • 1张妲,王昌惠,李强,郑建明,余永伟.胸腺瘤伴弥漫性泛细支气管炎一例报告并文献复习[J].中华结核和呼吸杂志,2004,27(9):608-610. 被引量：5
  • 2関根康雄.低γグロブリン血症(Good症候群).日胸,2007,66:105-108.
  • 3杉山幸比古.Good症候群とぴまん性汎細気管支炎.日胸,2007,66:130-136.
  • 4Azuma A, Kudoh S. Diffuse panbronchilitis in East Asia. Respirology, 2006,11:249-261.
  • 5神尾孝一郎,慶長直人.DPBにぉけるMHC関連疾患感受性遺传子.日胸,2002,61:582-589.
  • 6Good RA.Agammaglobulinaemia——a provocative experiment of nature.Bull Univ Minn,1954,26:1-19.
  • 7Kelleher P,Misbah SA.What is Good's syndrome? Immunological abnormalities in patients with thymoma.J Clin Pathol,2003,56:12-16.
  • 8Kelesidis T,Yang 0.Good's syndrome remains a mystery after 55 years:A systematic review of the scientific evidence.Clin Immunol,2010,135:347-363.
  • 9Tarr PE,Lucey DR.Good's syndrome:the association of thymoma with immunodeficiency.Clin Infect Dis,2001,33:585-586.
  • 10Miyakis S,Pefanis A,Passam FH,et al.Thymoma with immunodeficiency (Good's syndrome):review of the literature apropos three cases.Scand J Infect Dis,2006,38:314-319.

共引文献39

同被引文献23

  • 1Good RA. Agammaglobunemia: a provocative experiment of nature[ J]. Bull Univ Mimn Hosp Med Found, 1954, 26:1-19.
  • 2Pu C, Sukhal S, Fakhran S. Humoral immunity in bronehiectasis: finding Good' s syndrome [ J ]. Case Rep Pl.Lmonol, 2015,2015:531731. DOI: 10. 1155/2015/531731.
  • 3Souadjian JV, Enriquez P, Silverstein MN, et al. The spectrum of diseases associated with thymoma. Coincidence or syndrome.'? [J]. Arch Inter Med, 1974, 134(2) : 374-379.
  • 4Kelesidis T,Yang O. Good's syndrome remains a mystery after 55 yeares : a systematic review of the scientific evidence [J]. Clin Immunol, 2010, 135 (3):347-363. DOI: 10. 1016/i. clim. 2010.01. 006.
  • 5Kelleher P, Misbah SA. What is Good~ syndrome? Immunological abnormalities in patients with thymoma[ J]. J Clin Pathol, 2003, 56(1): 12-16.
  • 6Oritani K, Medina KL, Tomiyama Y, et al. Limitin: an interferon-like eytokine that preferentially influences B-lymphocyte precursors[ J ]. Nat Med, 2000, 6 (6) : 659-666. DOI: 10. 1038/76233.
  • 7Litwin SD, Zanjani ED. Lymphocytes suppressing both immunoglobulin production and erythroid differentiation in hypogammaglobulinaemia [ J ]. Nature, 1977,266 ( 5597 ) :57-58.
  • 8Chartes RJ, Sabo KM, Kidd PG, et al. The pathophysiology of pure red cell aplasia: implications for therapy[ J]. Blood, 1996, 87(11) : 4831-4838.
  • 9Tarr PE, Saeller MC, Mechanic LJ, et al. Infectious in patients with immunodeficiency with thymoma(Good syndrome). Report of 5 cases and review of literature[ J]. Medicine (Baltimore) ,2001, 80 : 123-133.
  • 10Orange JS, Grossman WJ, Naviekis R J, et al. Impact of trough IgG on pneumonia incidence in primary immunodeficiency: a meta-analysis of clinical studies[ J]. Clin Immunol, 2010, 137 ( 1 ) : 21-30. DOI: 10. 1016/j. clim. 2010.06. 012.

引证文献6

二级引证文献9

中华全科医师杂志
2014年 第4期

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