多囊肾合并内脏转位1例报告并文献复习

One case report of polycystic kidney disease with situs inversus and literatures review

目的:提高对多囊肾合并内脏转位的认识。方法:2012年3月我院收治1例多囊肾合并内脏转位患者,男,45岁,对其临床资料进行回顾性分析,同时复习相关文献。结果:患者因右侧腰部外伤就诊。肾功能示尿素氮13.1mmol/L、肌酐277μmol/L,B超和CT检查提示内脏转位、多囊肾、右肾及脾损伤。手术探查予以证实并行右肾和脾切除术。随访7个月,肾功能基本稳定。结论:多囊肾和内脏转位可根据影像学检查明确诊断。多囊肾可导致肾功能不全,目前尚无较好的治疗方法。内脏转位一般不需处理,但术前明确诊断可减少其他手术风险。

Objective： To improve the knowledge of polycystic kidney disease with situs inversus. Method： We reported a case of polycystic kidney disease with situs inversus who presented to our institution in March 2012. The clinical data of the 45-year-old male patient were analyzed retrospectively and the related literatures were re- viewed. Result： The patient presented with right flank pain after blunt right lumbar trauma. The level of blood u- rea nitrogen and serum creatinine were 13.1 retool/L, 277 μmol/L respectively. Ultrasonography and computer tomography （CT） suggested the diagnosis of situs inversus, polycystic kidney disease, and trauma of right kidney and spleen. Exploratory laparotomy confirmed the diagnosis and right nephrectomy and splenectomy were per- formed. During seven months follow-up, the patient＇s renal function was maintained at a normal level. Con.clusion： Imaging examination is helpful in diagnosing polycystic kidney disease with situs inversus. Polycystic kidney dis- ease can result in renal failure, and effective treatments still need investigating. Situs inversus may remain asymp- tomatie. However, management of patients with urologic disease requires careful preoperative evaluation to dimin- ish the possibility of operative risk.