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一例脊柱侧弯合并马凡氏综合征患者行矫形术的麻醉体会

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摘要 马凡氏综合征(Marfan’s Syndrome,MFS)俗称蜘蛛人症,是一种先天性遗传性结缔组织疾病,为常染色体显性遗传,有家族史。患者心脏、心血管可能发育异常,病变主要累及中胚叶的骨骼、心脏、肌肉、韧带和结缔组织,骨骼畸形最常见。
作者 陈燕 朱阿立
出处 《海南医学》 CAS 2014年第7期1044-1045,共2页 Hainan Medical Journal
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