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平山病的MRI表现及临床诊断价值 被引量:3

MRI Manifestation of Hirayama Disease and Its Diagnostic Value
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摘要 目的研究和总结平山病患者颈椎中立位和前屈位MRI的特点,探讨其对平山病诊断的价值。方法分析17例平山病患者颈椎中立位MRI低位颈髓形态、颈椎曲线、失连接(LOA)、脊髓内T2WI高信号;前屈位硬脊膜囊后壁前移、硬膜外间隙增宽伴流空信号等征象。结果颈椎中立位MRI低位颈髓萎缩、变扁10例(58.8%),颈椎曲线异常14例(82.4%),LOA征17例(100%),脊髓T2WI高信号影4例(23.5%);前屈位MRI硬膜囊后壁前移,低位颈髓受压17例(100%),硬膜外间隙增宽17例(100%),伴流空信号影16例(94.1%)。结论颈椎前屈位硬脊膜囊后壁前移、硬膜外间隙增宽伴流空信号、中立位LOA等征象具有明显的特征性,有很高的诊断价值。 Objective To study and summarize MRI manifestations of cervical spine obtained at flexion position and neutral position in patients with Hirayama disease, and to discuss the clinical value of these signs in making diagnosis. Methods A total of 17 patients with Hirayama disease were enrolled in this study. MR scanning was performed in all patients. The shape of lower cervical cord, the cervical curvature, the loss of attachment (LOA) and the intramedullary high signal intensity on T2-weighted images obtained at neutral position were analyzed. The anterior shifting of posterior dura matter, the widening of epidural space and the flow void signals demonstrated at flexion position were recorded. The results were analyzed. Results Neutral position cervical MR images showed that the lower cervical cord was atrophied and flat- tened in 10 cases (58.8%) , abnormal cervical curvature was found in 14 cases (82.4%), and LOA was seen in all 17 cases (100%). Intramedullary high signal intensity on T2-weighted MR images was detected in 4 cases (23.5%). Flex- ion position cervical MR images revealed that anterior shifting of posterior dura matter with lower cervical cord oppression as well as widening of epidural space could be found in all 17 cases ( 100% ), and flow void signals in epidural space could be seen in 16 cases (94.1%). Conclusion Several cervical MRI signs, such as anterior shifting of posterior dura matter, widening of epidural space and flow void signals in flexion position, LOA in neutral position, etc. are of great characteristics, which are very valuable in diagnosing Hirayama disease.
出处 《临床放射学杂志》 CSCD 北大核心 2014年第4期489-493,共5页 Journal of Clinical Radiology
关键词 平山病 运动神经元病 颈椎前屈位 颈椎中立位 磁共振成像 Hirayama disease Motor neuron disease Flexion-position cervical Neutral-position cervical Magneticresonance imaging
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参考文献17

  • 1Hirayama K, Toyokura Y,Tsubaki T. Juvenile muscular atrophy of u- nilateral upper extremity : a new clinical entity ( in Japanese ). Psy-chiatr Neurol Jpn, 1959,61:2190.
  • 2Hirayama K. Juvenile muscular atrophy of distal upper extremity ( Hirayama disease). Intern Med ,2000,39:283.
  • 3Chen C J, Hsu HL, Tseng YC, et al. Hirayama flexion myelopathy. Neutral-position MR imaging findings: importance of loss of attach- ment. Radiology ,2004,231:39.
  • 4Lin MS, Kung WM, Chiu WT, et al. Hirayama disease. J Neurosurg Spine ,2010,12:629.
  • 5傅瑜,樊东升,裴新龙,韩鸿宾,张俊,康德瑄.平山病的MRI诊断[J].中华放射学杂志,2007,41(4):352-355. 被引量:19
  • 6Hirayama K,Tokumaru Y. Cervical dotal sac and spinal cord in ju- venile muscular atrophy of distal upper extremity. Neurology, 2000, 54 : 1922.
  • 7曾丽莉,王瑛,陈晟,陈生弟,肖勤.平山病误诊运动神经元病二例临床分析[J].脑与神经疾病杂志,2010,18(4):294-296. 被引量:5
  • 8Eai V, Wong YC, Poon WL, et al. Forward shifting of posterior dural sac during flexion cervical magnetic resonance imaging in Hirayama disease: an initial study on normal subjects compared to patients with Hirayama disease. Eur J Radio1,2011,80 :724.
  • 9傅瑜,樊东升,裴新龙,韩鸿滨,张俊.自然位磁共振影像对平山病的诊断价值[J].中华内科杂志,2006,45(7):573-575. 被引量:37
  • 10Toma S, Shiozawa Z. Amyotrophic cervical myelopathy in adolea- cence. J Neurol Neurosurg Psychiatry, 1995,58:56.

二级参考文献44

  • 1邸旭辉,李娜,于绍斌,胡静.10例平山病肌电图特点分析[J].脑与神经疾病杂志,2008,16(6):700-702. 被引量:9
  • 2Fujimoto Y,Oka S,Tanaka N,et al.Pathophysiology and treatment for cervical flexion myelopathy.Eur Spine J,2002,11 (3):276-285.
  • 3Hirayama K.Juvenile muscular atrophy of distal upper extremity (Hirayama disease).Intern Med,2000,39(4):283-290.
  • 4Watanabe K,Hasegawa K,Hirano T,et al.Anterior spinal decompression and fusion for cervical flexion myelopathy in young patients.J Neurosurg Spine,2005,3(2):86-91.
  • 5Kohno M,Takahashi H,Ide K,et al.Surgical treatment for patients with cervical flexion myelopathy.J Neurosurg,1999,91 (1Suppl):S33-42.
  • 6Yaguchi H,Takahashi I,Tashiro J,et al.Scapular winging as a symptom of cervical flexion myelopathy.Intern Med,2007,46(8):511-513.
  • 7Masaki T,Hashida H,Sakuta M,et al.A case of flexion myelopathy presenting juvenile segmental muscular atrophy of upper extremities-a successful treatment by cervical spine immobilization.Rinsho Shinkeigaku,1990,30(6):625-629.
  • 8Ando T,Fukatsu H,Kameyama T,et al.A case of flexion myelopathy presenting with reversible muscular weakness and atrophy of the unilateral proximal upper limb.Rinsho Shinkeigaku,1993,33(5):575-578.
  • 9Tashiro K,Kikuchi S,Itoyama Y,et al.Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan.Amyotroph Lateral Scler,2006,7(1):38-45.
  • 10Hirayama K,Tokumaru Y.Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity.Neurology,2000,54(10):1922-1926.

共引文献61

同被引文献27

  • 1傅瑜,樊东升,裴新龙,韩鸿滨,张俊.自然位磁共振影像对平山病的诊断价值[J].中华内科杂志,2006,45(7):573-575. 被引量:37
  • 2傅瑜,樊东升,张俊,裴新龙,韩鸿滨,康德瑄.平山病的临床及颈磁共振成像影像学特点[J].北京大学学报(医学版),2007,39(2):189-192. 被引量:26
  • 3HASSAN K M,SAHNI H,et al. Nosology of juvenile muscular atrophy of distal upper extremity: from monomelic amyotrophy to Hirayama disease--Indian perspective[J]. Biomed Res Int,2013,2013( 1 ):478 516.
  • 4JAKHERE S, WAGH V. Hirayama's disease: the importance of flexion magnetic resonance imaging [J].Poslgrad Med,201 I ,57( 1 ):48--50.
  • 5HIRAYAMAK T OKUMARU Y. Cervical dural .sacand spinal cord injuvenlie M uscular atrophy of distal upper extemity [J].Neurology,2000,54(10):1922-1926.
  • 6MISRA U K,KAI,ITAJ,MISHRA V N,,fal. A clinical,magnetic. resonce imaging,and surval motor neuron gene deletion study of hirayama disease [J].Arch Neurol,2005,62(1):120-123.
  • 7YIN B,LIU L,(3ENG I) Y,et ill. Features of" Hirayama disease on fully flexed position 'elwical MRI[J ]. Jint Med Res,2011,39( 1 ):222--228.
  • 8札县半,张水顺.王建爽,等.平山病磁共振扫描技术探讨[J].医疗卫生装备,2010.31(4):337—339.
  • 9CHEN C J, HSU H L, TSENG Y C,e! al. Hirayama flexionmyelopalhy. Neulral --posilion MR imaging finding: impoutance of loss of atlachmenl[J]. Ra(lit)logy, 2004,231 (1):39--44.
  • 10CICERI E F, CHIAPPAIHNI Angiographically proven cervical wenou..ngowgement:a possihle concurrenl cause in Ihe palholhhysiohogy ofHirayama's myehopathy [J].Neural Sci.2010,31(6): 845--848.

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