布-加综合征的诊断与治疗(附46例临床分析)

Diagnosis and treatment of Budd-Chiari syndrome (clinical analysis of 46 cases)

目的探讨减少布 -加综合征的误诊误治措施。方法分析布 -加综合征 (Budd-Chiari syndrome) 46例的临床资料。结果 133例有误诊经过 ,平均误诊时间 5 .3年 ;2下肢病变为本病的主要表现 ,占 84.8% ;3彩色超声多普勒探查肝静脉及下腔静脉 ,10 0 %均有阳性征象发现 ,而误诊的病例均未做该项检查 ;4仅 4.3%患者的病毒标记为阳性 ,不超过一般人群阳性率。结论布 -加综合征症状多变 。

Objective To explore the measure to diminish the misdiagnosis of Budd Chiari syndrome.Methods 46 cases of Budd Chiari syndrome were analyzed.Results 33 cases had ever been misdiagnosed with average time of 5.3 years.One of the main clinical symptoms was the pathological process of lower limb (84.8%) .Doppler color flow imaging examination showed positive rate of 100% in liver veins and inferior vena cava,,but none of the misdiagnosed cases received this examination.The viral marker test had a positive rate of only 4.3% that was not higher than that of general population.Conclusion Budd Chiari syndrome has a variety of symptoms,so Doppler color flow imaging is considered an important means to diagnose this disease.