先天性肺动脉瓣缺如:附12例报告

Congenital absent pulmonary valve:A 12-cases' report

通过对少见的先天性肺动脉瓣缺如病例总结,提高认识其临床特征及内、外科诊断与治疗。12例病儿中除1例放弃治疗外,另11例均作心导管造影检查及外科手术,方法为肺动脉整形和/或用自体心包作右室流出道跨瓣补片。结果显示11例术前、后诊断一致。其中10例术后恢复良好,1例死亡。结果表明,通过及时的诊断与治疗,该病能获得较满意的疗效。

It was expected to improve the clinical cognition) medical and surgical diagnosis and treatment for absent pulmonary valve (APV), which was a kind of the relatively rare heart disease congenitally, by summarizing and analyzing 12 infants with APV during 1985-1999. There were 11 of 12 cases with APV accepted cardioangiographic examination and surgery with either the pulmonary arterial plication or a spanning-valve patch on the outflow tract of the right ventricle by using self-pericardium. The results showed that there was an accordant diagnosis before and after operation in all 11 cases. It is concluded that the satisfied effect can be obtained if patients with APV can be diagnosed and treated timely.