主动脉弓离断症2例报告

Interrupted Aoric Arch (Report of two cases)

主动脉弓离断症是一种较少见的先天性心血管疾病。常合并其他心内或心外畸形,以并发动脉导管未闭及室间隔缺损最为常见。本文报告2例,结合文献讨论病理分型、诊断及治疗方法。

Interrupted aortic arch is a rare congenital heart malformation frequently complicated by other extra or intracardiac cougenital defects. These anomalies are divided into three types, according to the site of the aortic interruption. The diagnosis may be suspected clinically in patients with diminished femoral pulses and when the partial pressure and saturation of oxygen in the blood from arteries proximal to the interruption are bighter than those from arteries distal to the interruption. The characters of heart murmurs are not of help in the diagnosis, which can be confirmed only by acsending aortogram. Surgical treatment, A two-stage approach has been routinely used in newborins. This operation consists of initial repair of the aortic interruption with leftsubclavian arteries (type A)or with a prosthetic tube (type B, C)and concomitant closure of the proximal end of the ductus by ligation or suturing to be fillowed by closure of the intracardiac defect at a later date. Correction of the interrupted aortic arch and intracardiac malformation can be done at one sitting in elder children.