表现为巨人症的垂体柄中断综合征1例
A case of pituitary stalk interruption syndrome with the manifestation of gigantism
摘要
垂体柄中断综合征(PSIS)是由于垂体柄缺如或纤细所致的以不同程度的垂体前叶激素分泌缺乏为主要临床表现的罕见疾病[1-2]。由于存在严重的生长激素缺乏,PSIS患者的身高常显著低于同龄人[3]。表现为巨人症的PSIS临床罕见。本文报道解放军第302医院内分泌科收治的表现为巨人症的PSIS患者1例,旨在提高对于该疾病的认识。
作者
杨彦
王煊
张婷婷
康姚洁
Yang Yan;Wang Xuan;Zhang Tingting;Kang Yaojie(Department of Endocrinology,Fifth Medical Center of PLA General Hospital,Beijing 100039,China)
出处
《国际内分泌代谢杂志》
2018年第6期429-432,共4页
International Journal of Endocrinology and Metabolism
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共引文献6
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