肝内胆管囊腺瘤的诊断与治疗进展

Advances in diagnosis and treatment of intrahepatic biliary cystadenoma

肝内胆管囊腺瘤是一种少见的肝囊性病变,具有恶性转化潜能,可转变为肝内胆管囊腺癌。该病多发生于中年女性患者(85%),常无特征性的临床表现,影像学检查可见肝内多发囊性病变,与肝囊肿、肝内胆管乳头状瘤等肝内其他囊性病变较难鉴别。该病漏诊率、误诊率高,最终诊断必须依靠病理学检查。手术完整切除肝内胆管囊腺瘤是该病的最佳治疗手段,术后患者可以获得良好预后。

Intrahepatic biliary cystadenoma (IBC) is a rare benign cystic neoplasm of liver, with malignant potential to transform into intrahepatic biliary cystadenocarcinoma. IBC predominantly occurs in women up to 85%, showing no special clinical symptoms and a polycystic lesion inside the liver on image examination. It is difficult to differentially diagnose from other cystic lesions of the liver such as simple liver cyst, intraductal papillary neoplasm of the bile duct, etc. The missed diagnosis and misdiagnosis rate were rather high in IBC, which is accurately diagnosed by pathological examination. Complete surgical removal of the tumor is the best way to cure it, and also can bring a satisfactory outcome to patients.