原发性胆汁性肝硬化并空肠间质瘤1例报道

Primary biliary cirrhosis with jejunal stromal tumor:one case report

原发性胆汁性肝硬化(primary biliary cirrhosis,PBC)是一种以胆汁淤积为特点的慢性自身免疫性肝病,常于疾病早期即可出现严重的门静脉高压。胃肠道间质瘤(gastrointestinal stromal tumour,GIST)因缺乏典型的症状,往往在其他疾病的诊疗过程中发现,首选手术治疗,门静脉高压通常增加了手术难度。本文报道了1例PBC合并空肠间质瘤的诊疗过程,供临床医师参考。

Primary biliary cirrhosis(PBC) is a chroic inflammatory autoimmune cholsetatic liver disease,which can occur severe portal hypertension in the early stage of disease.Gastrointestinal stromal tumor(GIST) are often found in the diagnosis and treatment of other diseases due to lack of typical symptoms,surgical resection is the primary treatment for GIST.Portal hypertension usually increases the difficulty of surgery.The paper reported one case of PBC with jejunal stromal tumor for clinical reference.