期刊文献+

鲁登巴赫综合征54例临床分析

Clinical analysis of 54 cases of Lutembacher’s syndrome
下载PDF
导出
摘要 目的:分析鲁登巴赫综合征(LS)的发病、超声特点和伴发病变,总结诊断及治疗经验。方法:回顾性分析武汉亚洲心脏病医院2008至2015年,诊治的鲁登巴赫综合征患者54例的临床症状、超声特点及诊治方法。结果:全组LS中,51例为经典性LS,3例为获得性LS,均合并不同程度肺动脉高压,绝大部分合并不同程度的三尖瓣关闭不全,少数合并主动脉瓣狭窄和关闭不全,亦有极少数合并永存左位上腔静脉和感染性心内膜炎。①全组病例有50例经超声心动图诊断,4例右心导管提示,2例术中诊断。②全组病例37例行外科治疗,1例行介入治疗,均无为手术期死亡,无严重心力衰竭、肺动脉高压危象及恶性心律失常发生。结论:LS的超声图像特征明显,超声心动图对其有特异性诊断价值;LS应及早手术或者介入治疗,修补或者封堵房间隔缺损同时有效解除或者减轻二尖瓣狭窄,探查并处理合并的三尖瓣关闭不全,可以取得满意的手术效果。 Objective: Aanalysis Lutembacher’s syndrome about the pathogenesis, ultrasonic features and complications, and to summarize the experience in diagnosis and treatment of Lutembacher’s syndrome. Methods: 54 patients with Lutembacher’s syndrome treated in Wuhan Asian Heart Hospital from 2008 to 2015 were analyzed retrospectively. Results: 51 cases were classic Lutembacher’s syndrome,3 cases were acquired Lutembacher’s syndrome, with different degree of pulmonary hypertension, most of them were complicated with tricuspid insufficiency, and a few cases were complicated with aortic stenosis and insufficiency. There are also very few patients with persistent left superior vena cava and infective endocarditis. ②50 cases were diagnosed by echocardiography, 4 cases were diagnosed by right cardiac catheterization and 2 cases were diagnosed intraoperatively. ③37 cases underwent surgical treatment and 1 case underwent interventional therapy, none of them died of operation, no severe heart failure, pulmonary hypertension crisis and malignant arrhythmia occurred. Conclusions: the sonographic features of Lutembacher’s syndrome are obvious, and echocardiography has specific diagnostic value. Early operation or interventional treatment should be performed to repair or block atrial septal defect and to relieve or alleviate mitral stenosis effectively. Exploration and treatment of combined tricuspid insufficiency can achieve satisfactory surgical result.
作者 严薇 马小静 何亚峰 YAN Wei;MA Xiaojiag;HE Yafeng(Depart-ment of Ultrasound,Wuhaa Asian Heart Disease Hospital,Wuhan 430022,China)
出处 《心肺血管病杂志》 2018年第12期1109-1112,1124,共5页 Journal of Cardiovascular and Pulmonary Diseases
关键词 鲁登巴赫综合征 超声心动图 诊断 治疗 Lutembacher's syndrome Echocardiography Diagnosis Treatment
  • 相关文献

参考文献7

二级参考文献68

  • 1应康,上官美琴,刘燕娜,郭良云,王继伟.超声心动图对风湿性二尖瓣狭窄经球囊扩张术远期疗效评价[J].江西医药,2013,48(4):297-299. 被引量:2
  • 2赵希武,杨耀晨,张显清.鲁藤巴赫综合征的外科治疗[J].中华胸心血管外科杂志,1994,10(2):145-145. 被引量:8
  • 3姜胜利,朱朗标,余翼飞,王冬青.鲁登巴赫氏综合征的诊断和治疗[J].中国循环杂志,1995,10(11):690-690. 被引量:4
  • 4周滔,沈向前,周胜华,祁述善,方臻飞,吕晓玲.经导管介入治疗鲁登巴赫综合征一例[J].中华心血管病杂志,2005,33(8):764-764. 被引量:2
  • 5John S,Menshi SC,Bhati ES,et al.Coexistent mitral valve disense with left-10-lihgt shunt at the atrial level,Results of sllrgical treaiment in 15 case.J Thorac Cardiovasc,1970,60:174.
  • 6Steinbrum W,Cohn KE,Selzer A.Atrial septal defect associated with Mitral stenosis.Am J Med,1970,48:295-297.
  • 7John S,Munshi SC,Bhati BS,et al.Coexistent mitral valve disease with left-to-right shunt at the atrial level.Results of surgical treatment in 15 cases.J Thorac Cardiovasc,1970,60:174.
  • 8Chen CH,Lin SL,Hsu TL,et al.Iatrogenic Lutembacher' syndrome after percutaneous transluminal mitral valvotomy.Am Heart J,1999,119:209.
  • 9Essop MR,Kontozis L,Sareli P.Preoperative left ventricular dysfunction correlates with the adverse postoperative consequences of annular-papilliar disconnection in the course of mitral valve replacement for stenosis.J Heart Valve Dis,1998,7:431-437.
  • 10Shigenobu M,Sano S.Evaluation of St.Jude Medical mitral valve function by exercise Doppler echocardiography.J Card Sung,1995,10:161-168.

共引文献16

相关作者

内容加载中请稍等...

相关机构

内容加载中请稍等...

相关主题

内容加载中请稍等...

浏览历史

内容加载中请稍等...
;
使用帮助 返回顶部