儿童肾上腺皮质癌九例报告

Clinical diagnosis and management of adrenocortical carcinoma in children

目的 提高儿童肾上腺皮质癌的诊断和治疗效果。 方法 回顾性分析 9例肾上腺皮质癌患儿资料。均为女性 ,左侧 5例 ,右侧 4例。 结果 行手术治疗 6例 ,其中姑息性切除 2例 ,肿瘤完整切除 4例 ;放弃治疗 1例 ,2例未及手术死于呼吸衰竭。手术 6例随访 3个月～ 5年 2个月 ,平均 2年 3个月。术后 2年无瘤生存 4例。 结论 早期发现、早期手术及完整切除肿瘤是提高儿童肾上腺皮质癌生存率的关键。

Objective To study the clinical features of adrenocortical carcinoma in children. Methods From 1983 to 1999, 9 cases of adrenocortical carcinoma were reviewed retrospectively. Results Six cases were surgically treated, complete tumor resection in four cases and palliative tumor resection in two.All were female. All the operated cases were followed up for an average of 2 years and 3 months.The 2 year survival is 4 out of 6. Conclusions Early diagnosis and complete tumor resection is the only means to achieve good survival in children with adrenocortical carcinoma.