二维及彩色多普勒超声诊断马凡综合征(附23例报告)

Two-Dimensional and Color Doppler Echocardiography in Diagnosis of Marfan's Syndrome

目的 分析马凡综合征心血管二维及彩色多普勒超声心动图特征 ,探讨其诊断价值。方法 2 3例马凡综合征患者进行经胸壁二维及彩色多普勒超声心动图多切面检查。结果 2 3例均显示升主动脉瘤及主动脉窦瘤、不同程度的主动脉瓣和 /或二尖瓣返流及左室扩大。 17例合并有主动脉夹层 ,其中A型 14例 ,B型 3例 ,与手术对照完全相符。结论 二维超声及彩色多普勒血流显像检查具有无创、操作快捷、重复性好等特点 。

Objective To analyze the characteristics of cardiovascular two-dimensional (2-D) and Color Doppler echocardiography for patients with Marfan's syndrome. Method 23 cases of Marfan's syndrome were examined by transthoracic 2-D and Color Doppler echocardiography.Results Aneurysms of the ascending aorta and aortic sinusal were found in all of these cases. Aortic regurgitation and left ventricular enlargement coexisted with all of these cases. Fourteen cases complicated with type A and three with type B aortic dissection. Conclusions 2-D and Color Doppler echocardiography is a rapid non-invasive,reproducible, comprehensive medical imaging technique and can be regarded as an initial imaging model to screen and diagnosis of Marfan's syndrome.