摘要
马德隆氏病是一种罕见的疾病,也称为良性对称性脂肪过多症(BSL),多发性对称脂肪堆积症(MSL),肥颈综合征或Launois-Bensaude综合征,其特征为多发性、对称性、脂肪组织松散地堆积在颈部、枕部、肩部、背部或胸部。脂肪组织是没有被包裹的,因此在相邻区域之间可以自由移动。这种疾病在地中海中年白人男子中最常见;在亚洲很少报道。马德隆氏综合征患者60?90%有慢性酗酒史。我们报告一例51岁中国男性酒精所致精神障碍患者,发现颈部脂肪组织3年里逐步扩展。根据病史、体格检查,颈部CT等常规检查结果,他被确诊为马德隆氏综合征。
Summary： Madelung＇s disease, also known as benign symmetric lipomatosis （BSL）, multiple symmetric lipomatosis （MSL）, fatty neck syndrome or Launois-Bensaude syndrome, is a rare disease characterized by the presence of multiple, symmetric, loose adipose tissues distributed around the neck, occipitalis, shoulder, back or chest. The fat masses are non-encapsulated and therefore can move freely between adjacent areas. This disease is most commonly seen among middle-aged Caucasian men of Mediterranean origins; it is rarely reported in Asia. Among individuals with Madelung＇s syndrome, 60 to 90% have a history of chronic alcohol abuse. We report a case of a 51-year-old Chinese man with a history of alcohol use disorder who had fat masses in his neck which gradually enlarged over a period of three years. Based on the case history and the results of physical examination, neck CT and other routine tests, he was diagnosed with Madelung＇s syndrome.
出处
《上海精神医学》
2014年第3期160-164,共5页
Shanghai Archives of Psychiatry
