先天性小睑裂综合征整复需关注的视功能问题

Pay attention to patient＇s visual function in oculoplastic surgery for congenital blepharophimosis syndrome

先天性小睑裂综合征指睑裂长度及宽度均较正常缩小,具有上睑下垂、小睑裂、反向内眦赘皮、内眦间距增宽等特征.其特有的眼部畸形,严重影响患者的外观,造成患者人格和心理发育障碍,只能通过手术矫正其畸形以改善外观.但此疾病不仅对患者外观而且对视功能亦有明显的影响,因此除美容整形外,还要考虑术后视功能的恢复.因此在术前应关注其对视功能的影响,术后及时进行弱视训练以帮助恢复视功能.另外,需综合考虑其解剖生理发育情况及其对视功能的影响程度,来决定手术时机并选择手术方式.

Blepharophimosis is characterized by the presence of a narrowed horizontal palpebral aperture,ptosis,epicanthus inversus,and telecanthus.Due to patient＇s eye deformity,both of hisorher appearance and psychological development are affected.In some cases,blepharophimosis not only influence the appearance but also the visual development.Therefore,patients with blepharophimosis require to be evaluated the visual function before the surgery in order to prevent amblyopia.In this article,we conclude that we should pay close attention to patient＇s visual function before and after the surgery.The timing of surgery must weigh the balance between early surgery to prevent amblyopia and late surgery for more reliable ptosis measurement,which provides a better surgical outcome.