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特发性间质性肺炎概念和分类的演变 被引量:8

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摘要 20世纪初,对慢性间质性肺疾病的大体病理和镜下病理已经有了较好的描述,当时对间质性肺疾病的研究重点是可能的职业和环境因素.1935年Hamman和Rich[1]首次描述了病因不明的爆发性间质性肺炎.1944两人报道了4例相似的患者,其特点均为急性起病,表现为发热、咳嗽和进行性呼吸困难,肺部为弥漫性的浸润影,病情进展迅速,均在短期内死亡,平均生存期仅1.7个月.肺组织病理表现为间质结缔组织弥漫性增生[2].伴单核细胞浸润的弥漫性间质纤维化因此成为弥漫性特发性纤维化性肺疾病的形态学特征.
作者 李海潮
出处 《中华结核和呼吸杂志》 CAS CSCD 北大核心 2014年第9期645-646,共2页 Chinese Journal of Tuberculosis and Respiratory Diseases
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