摘要
视网膜和视网膜色素上皮联合错构瘤（combined hamartoma of the retina and retinal pigment epithelium,CHRRPE）是一种少见的眼部良性肿瘤,可累及视盘、黄斑或周边视网膜,常见于儿童,其临床特征为瘤体位于视网膜,隆起,有不同程度的色素增生、血管迂曲及视网膜前膜形成.组织病理学检查显示CHRRPE主要由杂乱的胶质、视网膜血管及增生的视网膜色素上皮细胞构成.相干光断层扫描有助于本病的诊断,并可指导治疗.玻璃体切除联合视网膜前膜剥除术可在一定程度上恢复患眼的视网膜结构,稳定或提高视力。
Combined hamartoma of the retina and retinal pigment epithelium （CHRRPE） is a rare benign lesion in the macula,parapapillary,or peripheral retina that is commonly found in children.Clinical characteristics were elevation in retina,diferent degree of hyperpigmentation,retinal vascular tortuosity,as well as epiretinal membrane formation.Histopathologically,CHRRPE consists of disorganized glial tissue intermixed with numerous blood vessels and proliferating retinal pigment epithelium cells.Optical coherence tomography is a helpful tool in the diagnosis and management of CHRRPE.Pars plana vitrectomy with membrane peeling may result in restored retinal architecture to some extent and improved or stabled visual acuity for patients with CHRRPE.
出处
《国际眼科纵览》
2014年第4期268-272,共5页
International Review of Ophthalmology
