原发性淀粉样变性致巨大肝伴高尿酸血症1例报告
One case of hepatomegaly due to primary hepatic amyloidosis accompanied by hyperuricemia
摘要
患者,男性,55岁,主因“腹部胀痛、纳差1个月,症状加重伴双下肢水肿4 d”入院。入院前1个月无明显诱因出现腹部胀痛、纳差,为阵发性隐痛,腹胀呈进行性加重,饮食量较前明显减少,大便干燥,1次/3 d,偶尔大便表面带血,遂到某中心医院住院治疗。肝功能示:ALT 23 U/L,AST 49 U/L,GGT 742 U/L,ALP 295 U/L,白蛋白25.9 g/L。腹部 CT:(1)肝脏肿胀,脾稍大;(2)脾脏边缘中度强化团块影,局部隆起;(3)胆囊壁增厚,呈明显强化;(4)门静脉主干增粗,下腔静脉显影较淡;(5)腹腔积液。下腔静脉造影未见明显异常。给予对症治疗后腹胀缓解不明显,且逐渐加重,伴有双下肢水肿,为求进一步治疗转入本院。
出处
《临床肝胆病杂志》
CAS
2014年第10期1076-1077,共2页
Journal of Clinical Hepatology
基金
成都军区"十二五"计划面上项目(C14036)
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