摘要
目前原发性胆汁性肝硬化(primary biliary cirrhosis,PBC)的确切发病机制不明,其并发症多见,临床上报道的病例多为合并其他自身免疫性疾病,目前尚无合并布加综合征(BuddChiari syndrome,BCS)的报道,本文报道了3例PBC合并BCS的病例,并复习了PBC和BCS的发病机制、诊断、治疗的相关文献.
The exact pathogenesis of primary biliary cirrhosis is currently unknown. The complications of primary biliary cirrhosis are not rare, but most of them are other autoimmune diseases. Primary biliary cirrhosis with BuddChiari syndrome(BCS) is rarely reported. Here we report three cases of primary biliary cirrhosis with BCS. In addition, we performed a literature review to discuss the pathogenesis, diagnosis and treatment of primary biliary cirrhosis and BCS.
出处
《世界华人消化杂志》
CAS
北大核心
2014年第29期4543-4546,共4页
World Chinese Journal of Digestology