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开展胆道闭锁多中心研究的价值 被引量：13

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摘要 胆道闭锁（biliary atresia，BA）是以肝内、外胆管进行性炎症和纤维化梗阻为特征，导致肝内胆汁淤积、肝脏纤维化及硬化的病理过程，是婴儿期严重肝胆系统疾病之一，如不及时治疗，常在1岁左右死亡。胆道闭锁病因复杂，可能与遗传、免疫、病毒或其毒素介导等相关；基因突变与环境因素相互作用，促进BA发生及肝脏纤维化形成是其主要致病因素。
作者 詹江华 冯杰雄
机构地区 天津市儿童医院小儿外科 华中科技大学同济医学院附属同济医院小儿外科
出处 《临床小儿外科杂志》 CAS 2015年第1期1-3,共3页 Journal of Clinical Pediatric Surgery
基金 天津市卫生计生委攻关项目(项目号:14KG129)
关键词 胆道闭锁 多中心研究 肝内胆汁淤积 肝脏纤维化 价值 肝胆系统疾病 致病因素 病理过程
分类号 R726.5 [医药卫生—儿科]
  • 相关文献

参考文献19

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二级参考文献27

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  • 2罗义,郑珊.胆道闭锁术后胆管炎诊治的现代概念[J].临床小儿外科杂志,2006,5(2):113-116. 被引量：11
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共引文献73

同被引文献140

  • 1Hideaki Nakajima,Hiroyuki Koga,Manabu Okawada,Hiroki Nakamura,Geoffrey James Lane,Atsuyuki Yamataka.Does time taken to achieve jaundice-clearance influence survival of the native liver in post-Kasai biliary atresia?[J].World Journal of Pediatrics,2018(2):191-196. 被引量：6
  • 2王玮,郑珊,沈淳,肖现民.新生儿巨细胞病毒感染与胆道闭锁肝脏纤维化的相关研究[J].中华小儿外科杂志,2005,26(9):464-466. 被引量：28
  • 3Goda T, Kawahara H, Kubota A, et al. The most reliable early predictors of outcome in patients with biliary atresia after Kasai's operation[J]. J Pediatr Surg, 2013, 48 (12):2373- 2377.
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引证文献13

二级引证文献84

临床小儿外科杂志
2015年 第1期

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