生酮饮食疗法治疗癫癎新进展

Update on ketogenic diet therapies in epilepsy

生酮饮食（KD）最早用于治疗癫癎,近年来对难治性癫癎的治疗取得较好效果,特别是在Dravet综合征、Doose综合征、婴儿痉挛症、发热性感染相关癫癎综合征（FIRES）、结节性硬化症和局灶性皮质发育不良等顽固性、结构性癫癎等的治疗方面,有了更多的临床证据,尤其是KD能够改善认知、言语和行为问题,值得重视.

Although the ketogenic diet（KD） has originally been used to treat epilepsies,plenty of evidence about the efficacy to intractable epilepsy has not accumulated until recently.These epilepsy or epilepsy syndrome include：Dravet syndrome,Doose syndrome,infantile spasms,Angelman syndrome with epilepsy,tuberous sclerosis complex and focal cerebral dysplasia or other structural epilepsy.It is worth paying more attention to the efficacy of KD on cognition,language development and behavior problems.