婴儿法洛四联症外科根治手术

Surgical correction of Tetralogy of Fallot in infants

目的 总结我院对婴儿法洛四联症（TOF）外科治疗的结果和经验.方法 2009年1月至2014年8月,我院对156例婴儿TOF患儿进行Ⅰ期根治手术,年龄2～12个月,体重3～8 kg,男性106例,女性50例,其中有缺氧发作的36例,术前均经过心脏彩超和心脏螺旋CT检查确诊.手术均在中到深低温体外循环下进行,经右室或右房切口修补室间隔缺损,123例患儿行跨瓣环补片扩大右室流出道和肺动脉,同期完成其他合并畸形的矫治.结果 总住院病死率为7.69％（12例）,无Ⅲ度房室传导阻滞,右心室流出道轻度狭窄6例、中度狭窄3例、重度狭窄2例.结论 早期进行TOF根治手术可以取得良好的手术效果和相对低的手术病死率.

Objective To summerize some results and experience of the surgical treatment of Tetralogy of Fallot in infants. Methods From January 2009 to August 2009, 156 cases of infants with TOF including 106 cases of male, 50 cases of female, aged from 2-12 months, weight 3-8 kg, were undergone stage I radical surgery, in which 36 cases with hypoxic attack. The diagnoses were made by Doppler echocardiography and CT. The operations were carried out with moderate to deep hypothermic cardiopulmonary bypass. 123 cases of children required enlargement of outflow tract of right ventricle with transannular patch. Ventricular septa defect was repaired through the incision of right ventricle or right atrium, and at the same time the other combined deformity were treated. Results The hospital mortality rate was 7.69%（ 12 cases）, no Ⅲ degree atrioventricular block, right ventricular outflow tract mild stenosis 6 cases, moderate stenosis in 3 cases, severe stenosis in 2 cases. Conclusion Complete repair of Tetralogy of Fallut in infants is effective with relatively and lower hospital death rate.