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多发性肌炎/皮肌炎合并间质性肺疾病研究进展 被引量:3

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摘要 多发性肌炎(PM)/皮肌炎(DM)是一类以侵害骨骼肌为主的全身炎症性疾病,间质性肺疾病(ILD)是其常见的一种并发症,可按起病缓急分为两个亚类:急性/亚急性间质性肺炎(acute/subacute interstitial pneumonia,A/SIP)和慢性间质性肺炎(chronic interstitial pneumonia,CIP),其中A/SIP病情进展迅速,预后差,文献报道半年内生存率不足50%[1].现就PM/DM合并ILD的发病机制、自身抗体、治疗及预后等展开阐述.
出处 《中华内科杂志》 CAS CSCD 北大核心 2015年第11期983-986,共4页 Chinese Journal of Internal Medicine
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