头部皮肤再生不良9例临床分析

Clinical Analysis on 9 Cases of Aplasia Cutis Congenita

目的:分析头部皮肤再生不良的临床特点。方法:回顾分析9例头部皮肤再生不良患儿的临床资料,对其病史、皮损表现、预后等进行总结。结果:9例患儿中男4例,女5例,年龄1~6个月。皮损均表现为单发或多发的圆形脱发区,多发3例,单发6例。缺损面积:0.3 cm×0.3 cm^5 cm×4 cm。部位:顶部单发5例,枕部单发1例,顶部和枕部多发1例,顶部和额部多发2例。1例合并颅骨缺损,9例均未发现脑膜缺损。确诊后均采用保守治疗,目前随访皮损稳定。结论:头部皮肤再生不良需注意排查颅骨和脑膜的缺损情况;根据缺损的程度选择治疗方式,保守治疗是一种常用而有效的方法。

Objective： To investigate the clinical features of aplasia cutis congenita. Methods：Retrospective analysis was performed on clinical data from 9 patients with aplasia cutis congenital.Results： The 9 patients included 4 boys and 5 girls. Their ages ranged from 1 to 6 month-old. Lesions showed single or multiple circular alopecia patchy,which included 3 single defect and 6 multiple defects. Lesion areas was from 0. 3 cm × 0. 3 cm to 5 cm × 4 cm. Lesion sites of all the patients were 5 on parietal only,1 on occipital only,1 on parietal and occipital with multiple lesions,2 on parietal and frontal with multiple lesions. The skull defect was involved in 1 patient and no meninges defect was found in any of the patients. They all received conservative treatment,and all lesions were stable during the follow-up. Conclusion： Carefully examination of the defect of skull and meninges should be carried out when we meet patients with aplasia cutis congenita. Appropriate treatment should be selected according to the degree of scalp defect. Conservative treatment is a common and effective method.