腹膜后肾上腺外副神经节瘤的临床表现及影像学分析

Clinical manifestations and imaging features of the retroperitoneal extraadrenal paraganglioma

目的:分析腹膜后肾上腺外副神经节瘤患者的临床资料及影像学表现,旨在增强对该病的认识,提高其术前诊断的准确性。方法:回顾性分析27例经病理学证实的腹膜后肾上腺外副神经节瘤的临床及影像学资料。结果:24例患者病灶为单发,功能性肿瘤19例中血压增高者16例。26例患者病灶为良性,呈椭圆形或类圆形,边界清楚;1例恶性,侵犯邻近下腔静脉。平扫肿瘤质地多不均匀,瘤内见出血、坏死或囊变,动态增强扫描显示大部分病灶实质性成分强化显著,部分区域动脉期强化程度与血管接近,2例肿瘤呈延迟强化。结论:腹膜后肾上腺外副神经节瘤具有一定的影像学特征,与临床特点相结合,能提高其术前诊断的准确性。

Objective： To analyze the clinical manifestations and imaging features of the retroperitoneal extraadrenal paraganglioma in order to enhance the understanding of the disease and improve the accuracy of preoperative diagnosis. Methods： The clinical characteristics and imaging features of 27 patients with pathologically proven retroperitoneal extraadrenal paraganglioma were retrospectively analyzed. Results： Single tumor was found in 24 patients,functional tumors were found in 19 patients,including 16 with increased blood pressure. The benign tumors were oval or circular with well-defined margin in 26 cases,while the only one malignant tumor involving the neighboring inferior vena cava. On plain CT,the texture of the tumors was uneven with hemorrhage,necrosis or cystic degeneration. On dynamic contrast-enhanced scan,the solid part of the most tumors showed marked enhancement,some similar to vessel enhancement,while 2 cases had delayed enhancement.Conclusion： The retroperitoneal extraadrenal paraganglioma has its imaging characteristics,whose accuracy of preoperative diagnosis can be improved if combined with the clinical features