丛状纤维组织细胞瘤3例临床分析

Clinical analysis on 3 cases of plexiform fibrohistiocytic tumor

目的探讨丛状纤维组织细胞瘤临床表现、病理特点、治疗方法及预后。方法回顾性分析中国人民解放军总医院2000年至2015年收治的3例丛状纤维组织细胞患者病历资料并复习文献。结果 3例患者经手术治疗,2例患者经常规扩大切除现无复发,1例患者首次治疗未按恶性肿瘤行扩大切除术,术后复发,3例均无远处转移。结论丛状纤维组织细胞瘤是一种罕见肿瘤,临床及病理诊断均易误诊,虽属低度恶性肿瘤,手术治疗仍需按常规恶性肿瘤原则切除,否则也有复发可能。

Objective To investigate the clinical manifestations, the physiological characteristics, the therapeutic methods and the prognosis of Plexiform Fibrohistioeytie Tumor. Methods The case data of 3 cases of Plexiform Fibrohistiocytic Tumor admitted to the Chinese People＇s Liberation Army General Hospital from 2000 to 2015 retrospectively analyzed and the literatures were reviewed. Results All the three cases were surgically treated. No recurrence has been observed up to now in 2 cases treated by regular extended resection. And one case was not treated by regular extended resection for malignant tumors at the time of the first treatment and recurrence was observed after the operation. No distant metastasis was observed in any of the 3 cases. Conclusion Plexiform Fibrohistiocytic Tumor is a kind of rare tumor. Mis-diagnosis is very likely both clinically and pathologically. Although it is a kind of low grade malignant tumor, regular malignant tumor resection shall be performed when it is treated surgically, or recurrence can be possible.