探讨Weill—Marchesani综合征继发青光眼的手术治疗

Surgery for treating secondary glaucoma in Weill-Marchesani syndrome

目的探讨魏尔-马切桑尼综合征（Weill．Marchesani syndrome，球形晶状体-短指综合征）继发青光眼手术治疗的最佳方式。方法回顾分析我院双眼Weill—Marchesani综合征继发青光眼1例，两眼先后采用不同的治疗方式，一眼行晶状体吸出联合小梁切除术、二期前部玻璃体切除联合人工晶状体悬吊术，另眼行晶状体及前部玻璃体切除联合人工晶状体悬吊术。以眼压为指标，随访2年。结果右眼晶状体吸出联合小梁切除术后不能顺利植入人工晶状体，二期前部玻璃体切除联合人工晶状体悬吊术后出现低眼压情况；左眼晶状体及前部玻璃体切除联合人工晶状体悬吊术后眼压正常且稳定。结论晶状体及前部玻璃体切除联合人工晶状体悬吊术是控制Weill—Marchesani综合征继发青光眼眼压的有效手术方式。

Objective To investigate the best operation for secondary glaucoma in Weill- Marchesani syndrome. Methods One patient of bilateral Weill-Marchesani syndrome with secondary glaucoma in our hospital was retrospectively analysed. The right eye received extraction of lens combined with trabeculectomy and second-stage operation of anterior vitrectomy combined with intraocular lens suspension. The left eye received lensectomy and anterior-vitrectomy combined with intraocular lens suspension. The intraocular pressure was measured at different times within two years. Results After extraction of lens combined with trabeculectomy, the intraocular lens could not be implanted into the right eye, and low intraocular pressure occurred after second-stage operation of anterior-vitrectomy combined with intraocular lens suspension. In the left eye normal intraoeular pressure was gained after lensectomy and anterior vitrectomy combined with intraocular lens suspension surgery. Conclusion Lensectomy and anterior vitrectomy combined with intraocular lens suspension surgery may be effective for secondary glaucoma in Weill-Marchesani syndrome.