LVAS与耳蜗发育状态及CI术后效果分析

Analysis of the Development of Cochlear in Large Vestibular Aqueduct and Effects after Cochlear Implantation

目的探讨大前庭水管畸形与耳蜗发育不良之间的关系,对人工耳蜗植入术（cochlear implantation,CI）后效果进行分析。方法自2001年6月～2015年12月间,对426例颞骨高分辨率CT（high resolution CT,HRCT）诊断为大前庭水管畸形的行CI患者的耳蜗发育状况行影像学的测量,与正常耳蜗的形态相比较,分析大前庭水管畸形与耳蜗发育状态的形态学关系,并将大前庭水管畸形伴耳蜗发育不良程度进行CI术后的听觉、言语效果的比较、分析。结果经CI证实,426例大前庭水管畸形均伴有伴耳蜗发育不良,其中耳蜗顶圈缺如354例,占83%,耳蜗发育不足小于2圈大于1.5圈者72例,占17%。79例术中出现＂井喷＂,占18.5%。结论 1本组426例大前庭水管畸形均存在耳蜗发育不全。2大前庭水管综合征的CI术后效果有差异与耳蜗发育不全的程度关系密切。

Objective To study the relationship between the large vestibular aqueduct（LVA） and cochlear malformation,and analysize the postoperative effects after cochlear implantation（CI）. Method 426 recipients of CI with 1arge vestibular aqueduct syndrome（LVAS） diagnosised by high resolution CT（HRCT） were measured and the relation of LVA to cochlear malformations was analyzed by comparing with nomal cochlea from June,2001 to December,2015.The effects of postoperative hearing, language degree of LVAS with cochlear dysplasia were compared and analyzed, too. Results Confirmed by CI, all the recipients were with dysplasia of the cochlea.There were 354 cases whose apical turn was absent, accounting for 83%. There were 72 cases whose cochlear developed less than 2 turns,accounting for 17%.In addition, there were 79 cases found perilymphatic ＂gusher＂in CI, accounting for 18.5%.Conclusion In our study, 426 recipients of LVAS were all with partly cochlear dysplasia. It was nearly 1/5 that osseous internal auditory canal fundus was incomplete and connected with inner ear abnormally. The different effects of these patients after CI lied in the extent of the cochlea dysplasia.