摘要幼年性透明性纤维瘤病（juvenile hyal ine fibromato-sis,JHF）是一种罕见的结缔组织常染色体隐性遗传病。本病以皮肤丘疹结节,皮下结节,伴齿龈肥大、溶骨及屈曲挛缩为特征。全世界目前报告仅40余例,国内1998年首次报告。2014年12月,我科收治1例幼年性透明性纤维瘤病患者,经积极治疗与精心护理,效果满意。现将围术期护理体会报告如下。
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