党中勤教授治疗肝性血卟啉病验案赏析

Analysis on Proven Cases of Professor Dang Zhongqin in the Treatment of Hepatic Porphyria

肝性血卟啉病临床较为少见,凡遇原因不明的阵发性腹痛,腹痛剧而压痛轻,伴有黄疸、便秘、尿色黄赤,尤其是青年女性患者,应考虑此病,查尿卟胆原(PBG)试验可确诊[1]。党中勤教授认为湿热阻滞、瘀血内结为本病最根本的病因,治以利湿退黄、活血祛瘀为主,佐以健脾理气,采用中药内服并中药灌肠等特色疗法,收到满意疗效。

Hepatic porphyria is rare in clinic, where in case of unknown causes of paroxysmal abdominal pain, abdominal pain show-ing mild tenderness, accompanied by jaundice, constipation, urine color, red, yellow, especially young female patients, and the disease should be considered. The urinary porphyrin bile original（ PBG） test can be used to diagnose. Professor Dang Zhongqin thought that heat block and blood stasis within the node was the most fundamental etiology of the disease. The tratment was mainly damp jaundice, promoting blood circulation and removing blood stasis, accompanied by invigorating spleen and regulating qi. The traditional Chinese medicine oral administration and traditional Chinese medicine enema characteristic therapy received satisfied curative effect.