腹茧症病因及诊治的研究进展

Pathogenesis, diagnosis and treatment progress of abdominal cocoon syndrome

腹茧症以小肠被茧状包裹在一层异常的质韧纤维膜内为其特征,伴随腹膜的主要变化特点为腹膜不断增厚硬化,进而逐渐缩窄,超滤能力下降,导致小肠部分或完全梗阻。该病的病因尚不十分清楚,临床症状缺乏特异性,术前诊断很困难,多在术中或尸检中偶然发现,手术难度极大,术中损伤几乎难以避免。因此,提高对该病的认识和治愈率显得至关重要,本文就此做一综述。

Abdominal cocoon syndrome is characterised by that the small intestine is wrapped in a layer of fiber membrane of anomalies, with major changes of peritoneal thickening, hardening, and then gradually being narrowed, and loss of ultrafiltration, leading to partial or complete intestinal obstruction. The pathogenesis and clinical manifestation of AC is nonspecific;therefore, preoperative diagnosis is difficult. Most cases are accidentally discovered intraoperatively or during autopsy, since surgery is difficult to be scheduled. It is more important to deepen the understanding and improve the cure rate of this disease.