以顽固性胸腔出血为表现的肺上皮样血管肉瘤1例

One case of pulmonary epithelioid angiosarcoma with refractory pleural hemorrhage

肺上皮样血管肉瘤(PEA)非常罕见,仅见个案报道。目前病因不明确,尚无统一的治疗标准,化疗及放疗都不敏感,临床表现多样,诊断困难。本文介绍1例以顽固性胸腔出血为表现的PEA病例的临床表现、病理、治疗经过及病情进展,进一步加深对该疾病的认识。PEA病理提示广泛出血,发病时有咯血及多发转移者预后极差。

Pulmonary epithelioid angiosarcoma is a kind of malignant tumor which is derived from blood vessel and very rare in clinic,only case reports.The etiology is not clear,it has no unified standard treatment and is not sensitive to chemotherapy and radiotherapy.Because of the variety of clinical symptoms,it is difficult to diagnosis.1 case of pulmonary epithelioid angiosarcoma with refractory pleural hemorrhage was reported in this paper,in order to provide more clinical information and improve the understanding of the disease.Once pathological prompt extensive hemorrhage,hemoptysis,multiple transfer and the prognosis would be very poor.