肺淋巴管肌瘤病的HRCT分析

目的 探讨肺淋巴管肌瘤病HRCT表现特征及其诊断价值。方法：回顾分析10例经胸腔镜或穿刺活检病理证实的肺淋巴管肌瘤病患者的cT资料，对病变的cT征象进行分析。结果：常规cT扫描见两肺，“泛或散在分布的小囊状影：HRCT上表现为两肺薄鼙小囊状影，病灶之间可见止常肺组织。病变分布无规律性，大小不一，随病程进展，病变增多、增大，并可融合成肺大泡，可形成气胸。2例伴有双肾错构瘤，1例合并纵隔内淋巴结肿大。结论：肺淋巴管肌瘤病HRCT表现具有特征性，HRCT对本病诊断及鉴别诊断有重要价值。

Objective Exp lore the characteristics and diagnostic value of pulmonary HRCT findings lymphangiomyomatosis.Methods：Retrospective analysis of 10 cases of thoracoscopic or needle biopsy of lung lymphangiomyomatosis patients with CT data, signs of lesionsanalyzed CT.Resuhs： Conventional CT scan showed both lungs or widely scattered small cystic shadow distribution; thin-walled lungs showedsmall cystic shadow on HRCT, visible between normal lung tissue lesions. Irregular distribution of lesions, large and small, with diseaseprogression, lesions increased, increased, and can be integrated into the bulla, can form a pneumothorax. Two cases with renal angiomyolipoma.Conclusion：Lung lymphangiomyomatosis HRCT findings with the characteristic, HRCT diagnosis and differential diagnosis of this disease hasimportant value.