头颈部软组织韧带样纤维瘤病的MRI表现

MR Imaging Features of Soft Tissue Desmoid-Type Fibromatosis in the Head and Neck

目的探讨头颈部软组织韧带样纤维瘤病的MRI表现。方法回顾性分析经病理证实的11例头颈部韧带样纤维瘤病的MRI表现,分析肿瘤的位置、形态、大小、边界、信号强度及增强的特点。结果 11例韧带样纤维瘤病患者中,病灶位于椎旁间隙5例,颈动脉间隙4例,咀嚼肌间隙1例及下颌下间隙1例,最长径2.6~16.1cm,其中8例沿肌间隙呈狭长状生长,6例病灶边缘见脂肪环征。10例病灶在T1WI上呈等或稍低信号、T2WI上呈稍高或高信号为主,内部均见条状、束状或分隔状低信号影,增强扫描病灶明显强化,其内低信号影无强化。另1例病灶在T1WI及T2WI上均呈低信号,增强扫描无强化。所有病例均未见明显坏死,除1例复发病例外周围肌肉均未见水肿。结论头颈部软组织韧带样纤维瘤MRI表现有一定特征,多数病例术前能做出正确诊断。

Objective To study the MR imaging features of soft tissue desmoid-Type fibromatosis in the head and neck.Methods 11 cases of soft tissue desmoid-type fibromatosis in the head and neck,which were confirmed by pathology,were analyzed retrospectively. The tumor location,morphological features,size,margins,intensity and contrast enhancement characteristics were assessed. Results In all 11 cases of desmoid-type fibromatosis,the lesions that were located in the perivertebral space（ n = 5）,carotid space（ n = 4）,submandibular space（ n = 1） and masticator space（ n = 1）. the greatest dimension ranges from 2. 6 cm to 16. 1 cm,8 cases grew in the Muscular clearance with an elongated shape,and rim of surrounding fat（ n = 6）. 10 cases showed iso-intense or slight hypo-intense signal on T1-weighted image and high or slight high signal on T2-weighted image,with marked enhancement. Characteristic nonenhancing low signal intensity bands can be seen in the 10 cases. 1 case of lesions was low signal on both T1WI、T2WI and enhancement. Necrosis was not found in all lesions except one recurrence case. Edema was not seen in muscles. Conclusion Desmoid-type fibromatosis in the head and neck have some certain characteristics. Most cases can be accurately diagnosed preoperatively.