儿童脂肪母细胞瘤病3例报告并文献复习

Analysis of lipoblastomatosis and review(report 3 cases).MO

目的探讨脂肪母细胞瘤病的临床特点及诊疗方式。方法回顾性分析2011年12月至2014年4月在本院住院治疗的3例脂肪母细胞瘤病患儿的临床资料,3例均为男性,年龄分别为1岁3个月,4岁6个月,12岁1个月,平均5岁11个月。患儿均以无痛性肿物就诊。结果 3例患儿均行手术治疗,1例接受2次手术。术后病理诊断脂肪母细胞瘤病。随访平均约1年,无死亡病例,1例未复发,2例仍有残留或者复发。结论脂肪母细胞瘤病多表现为无痛性肿物,治疗为手术切除,但手术难切除干净,复发率很高,需要长期随访。

Objetive To explore the clinical characteristics and diagnosis and treatment of lipoblastom-atosis. Methods A retrospective analysis was made on 3 children with lipoblastomatosis in our hospital.All cases were male,aged from 1 year and 3 months to 1 2 years and 1 month,with the average age of 5 years and 1 1 months.All cases were with painless mass. Results All operations went well.The definite diagnosis of li-poblastomatosis were determined by pathology in 3 cases.Patients were followed up about 1 year,finding 1 case without recurrence and 2 cases with recurrence. Conclusions Lipoblastomatosis patients are usually with painless mass.The efficient treatment of lipoblastomatosis is operation.But it is difficult to remove the whole tumor,and it also has a high recurrence rate.It needs to be followed up for a long time.